〔EC 6.4.1.1〕丙酮酸羧化酶：为连接酶之一种，催化ATP＋丙酮酸＋HCO3＝ADP＋正磷酸盐＋草酰乙酸的不可逆反应。此酶为一生物素基性蛋白质，需要Mg＋＋或Mn＋＋和乙酰辅酶A，在肝内而不在肌肉内产生。此反应是由乳酸或氨酸异生葡糖以生成丙酮酸所必需的，并为三羧酸循环提供四碳化合物。此酶缺乏(常染色体隐性遗传)可致婴儿严重精神运动性阻滞和乳酸性酸中毒- hypovarianism
- hypovenosity
- hypoventilation
- hypovitaminosis
- hypovolemia
- hypovolemic
- hypovolia
- hypoxanthine
- hypoxanthine guanine phosphoribosyltrans-ferase
- hypoxanthine guanine phosphoribosyltrans-ferase (HGPRT, HPRT) deficiency
- hypoxanthine oxidase
- hypoxanthine phosphoribosyltransferase (HP-RT)
- hypoxemia
- hypoxia
- hypoxic
- hypoxidosis
- HypRho-D
- hypsarhythmia
- hypsarrhythmia
- hypsi-
- hypsibrachycephalic
- hypsicephalic
- hypsicephaly
- hypsiconchous
- hypsiloid