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单词
aminobutyrate aminotransferase
释义
aminobutyrate aminotransferase
〔EC 2.6.1.19〕氨基丁酸转氨〔基〕酶:属转移酶类,催化反应为4-氨基丁酸+2-酮戊二酸=琥珀酸半醛+L-谷氨酸;反应主要在脑内神经元中进行。还可作用于β-氨基丙酸(β-丙氨酸),生成丙二酸半醛。此酶的先天性缺乏(属常染色体隐性遗传)可致高β-氨基丙酸血症
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更新时间:2025/5/25 3:59:30