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单词
N-acetylglucosamine-6-sulfatase
释义
N-acetylglucosamine-6-sulfatase
〔EC 3.1.6.14〕N-乙酰葡〔萄〕糖胺-6-硫酸酯酶:属水解酶类,促使硫酸乙酰肝素及硫酸角质素中N-乙酰-D-葡糖胺-6-硫酸基团水解,为硫酸乙酰肝素降解过程中的一步,此酶缺陷为常染色体隐性遗传,引起D型Sanfilippo综合征
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更新时间:2025/9/4 16:43:48