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单词
α-D-galactosidase
释义
α-D-galactosidase
α-D-半乳糖苷酶:一种水解酶,催化在α-D-半乳糖苷中的末端非还原α-D半乳糖残基的水解
习惯用语
  
α-D-g.A
α-D-半乳糖苷酶A:不耐热溶酶体酶,催化下列反应:神经酰胺-葡萄糖-半乳糖-半乳糖+H2O=神经酰胺-葡萄糖-半乳糖+半乳糖。缺乏该酶(X连锁遗传)将导致血浆和组织中神经酰胺三己糖苷的蓄积,临床表现为弥漫性血管角化病(见disease项下的Fabrys disease)
  
α-D-g.B
α-D-半乳糖苷酶B:同α-N-acetylgalactosaminidase
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更新时间:2025/5/29 2:39:19