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α-glucosidase
释义
α-glucosidase
〔EC 3.2.1.3,3.2.1.20〕α-葡糖苷酶:一种水解酶,催化末端非还原性1,4-连接α-D-葡萄糖残基的水解(这种残基主要在低聚糖分子上,亦可在多糖分子上),并释出α-D-葡萄糖。溶酶体(酸性)α-葡糖苷酶缺乏(为常染色体隐性性状)导致糖原贮积症Ⅱ型(Pompe病)
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lysosmal α-g.
溶酶体α-葡糖苷酶:即葡聚糖-1,4-α葡糖苷酶(glycan-1,4-α-glucosidase)
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更新时间:2025/9/3 2:40:17