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单词
α-ketoglutarate glyoxylate carboligase
释义
α-ketoglutarate glyoxylate carboligase
α-酮戊二酸乙醛酸醛连接酶:催化反应为乙醛酸+α-酮戊二酸=α-羟-β-酮己二酸+CO2。此反应需焦磷酸硫胺素。缺乏此酶可引起原发性I型高草酸盐尿,为常染色体隐性遗传
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更新时间:2025/9/3 2:46:41