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单词
N-sulfoglucosamine sulfohydrolase
释义
N-sulfoglucosamine sulfohydrolase
N-磺基葡萄糖胺磺基水解酶:催化N-磺基-D-葡萄糖胺+水=D-葡萄糖胺+硫酸反应的水解酶。该酶可能与催化乙酰肝素中的葡萄糖胺硫酸盐单位(glucosamine sulfate units)水解的乙酰肝素N-硫酸酯酶(heparan N- sulfatase)相同,缺乏该酶会导致A型Sanfilippo综合征(Ⅲ型粘多糖病)
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Bergenhem's operation
Bergeron's chorea(disease)
Berger rhythm
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Bergmann's incision
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Bergonié-Tribondeau law
beriberi
beriberic
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Bernard-Soulier disease(syndrome)
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Bernhardt-Roth disease,syndrome
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Bernheimer's fibers
Bernoulli distribution,trial
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更新时间:2025/5/25 17:43:45